Titlebook: Orphan Lung Diseases; A Clinical Guide to Vincent Cottin,Luca Richeldi,Francis X. McCormack Textbook 2023Latest edition The Editor(s) (if

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Eosinophilic Granulomatosis with Polyangiitistly affects small- and medium-sized vessels and is characterized by asthma and blood eosinophilia [1, 2]. Although anti-neutrophil cytoplasm antibody (ANCA) presence is not constant, EGPA is classified as a small-sized vessel, ANCA-associated vasculitis (AAV) [3]. Clinical phenotypes and pathogenic

听写

Granulomatosis with Polyangiitisis also one of the three classical vasculitides associated with anti-neutrophil cytoplasm antibodies (ANCAs), along with microscopic polyangiitis and eosinophilic granulomatosis with polyangiitis. The incidence rate of GPA varies depending on the studies and countries between 2 and 30 cases per year

Carcinogenesis

Alveolar Hemorrhagen. Patients commonly present with dyspnea, hemoptysis, anemia, diffuse radiographic pulmonary infiltrates, and hypoxemia. The severity can range from mild dyspnea to severe hypoxemic respiratory failure requiring mechanical ventilation. Diagnosis is frequently made at the time of bronchoscopy, when

Kaleidoscope

Pulmonary Involvement in Takayasu Arteritis and Behçet Diseased blood vessels, and pathologically by the nature of the cellular infiltrate. Vasculitic involvement of pulmonary blood vessels may be secondary to infectious diseases, connective tissue diseases, malignancies, and hypersensitivity disorders or can be seen as a feature of primary small-vessel antine

habitat

Portopulmonary Hypertension and Hepatopulmonary Syndromechronic liver disease. Despite being uncommon, these conditions have significant prognostic and therapeutic implications for patients, particularly those considering liver transplantation (LT). Mechanisms of disease pathogenesis in PoPH and HPS are poorly understood but involve vasoactive mediators

Proclaim

完成

CEDE

Lung Disease in Systemic Lupus Erythematosus, Myositis, Sjögren’s Disease, and Mixed Connective Tissmatosus (SLE), Sjögren’s syndrome (SS), and Mixed Connective Tissue Disease (MCTD) can affect different levels of the respiratory tract, with a wide range of symptoms intensity, from asymptomatic to severe or life-threatening forms. Pleural disease is the most common lung manifestation in SLE and MC

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