Titlebook: Cystic Fibrosis; A Multi-Organ System Stephanie Duggins Davis,Margaret Rosenfeld,James C Book 2020 Springer Nature Switzerland AG 2020 cyst

Confound

Maintenance of Pulmonary Therapiesatment regimens. In addition, clinical practice guidelines have been developed worldwide to standardize the treatment of CF pulmonary disease and updated to include the CFTR modulator therapies. How the CFTR modulator therapies might alter the present recommendations for maintenance pulmonary therap

敌意

Lung Transplantation for Cystic Fibrosist. Early discussion regarding transplant as a treatment option is critical to maximizing opportunity and optimizing patient and family experience. The decision to be evaluated for transplant and to list for transplant are distinct, and early referral and evaluation may provide a treatment option tha

发源

Hepatobiliary Involvement in Cystic Fibrosisons develop, and because serum liver enzymes are often nonspecifically elevated in CF, annual screening for structural liver disease is recommended. Once the diagnosis is established, treatment with ursodeoxycholate is often advised, although evidence for its efficacy remains a subject of discussion