clarify
发表于 2025-3-23 12:57:30
Disorders of Fatty Acid Oxidationhreatening episodes of hypoketotic, hypoglycemic coma induced by fasting . In some of the disorders, there may also be chronic skeletal-muscle weakness or acute exercise-induced rhabdomyolysis and acute or chronic cardiomyopathy. Recognition of the fatty acid-oxidation disorders is often diffic
放逐某人
发表于 2025-3-23 15:34:00
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上下连贯
发表于 2025-3-23 19:01:48
Defects of the Respiratory Chaintricted to the neuromuscular system but proceeds in all cells that contain mitochondria (Fig. 13.1). Most non-neuromuscular organs and tissues are, therefore, also dependent upon mitochondrial energy supply. Therefore, due to the twofold genetic origin of respiratory enzymes [nuclear DNA and mitocho
Inexorable
发表于 2025-3-24 02:02:44
The Hyperphenylalaninaemiaste normal ranges for blood concentrations: phenylalanine 35–120 μmol/1; tyrosine 40–130 μmol/1). Hyperphenylalaninaemia arises due to a block in the conversion of phenylalanine into tyrosine due to a defect in either the enzyme phenylalanine hydroxylase (98% of subjects) or in the metabolism of the
abject
发表于 2025-3-24 05:34:01
Disorders of Tyrosine Metabolismver disease and renal tubular dysfunction with rickets. Hereditary tyrosinaemia type II (Richner-Hanhart syndrome) presents with keratitis and blisterous lesions of the palms and soles. Tyrosinaemia type III may be asymptomatic or associated with mental retardation. Hawkinsinuria may be asymptomatic
Irremediable
发表于 2025-3-24 07:10:17
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矛盾
发表于 2025-3-24 12:36:01
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不如乐死去
发表于 2025-3-24 17:00:53
Georges Van den Berghesure that their marketing spend produces reasonable returns. In my view, the field still lacks comprehensive models to link marketing spending and customer action. A number of customer-management authorities have developed customer life-cycle planning with conceptual notions of customer journey. Pro
仪式
发表于 2025-3-24 22:12:45
Pascale de Lonlay,Jean-Marie Saudubrayegy. Traditional strategy development process applies tools and concepts like mission (defining the company’s purpose), vision (inspiring future results) and value statements to guide the company’s strategy development. However, due to changes and competition, a company cannot thrive by its internal
engender
发表于 2025-3-25 00:01:54
equently, the product-mix of companies, spread across the product categories and product lines, are stuffed with a variety of brands with marginal differentiation. Such business situations exhibit chaos of brands within the product line triggering cannibalization of brands within the product line of