温顺 发表于 2025-3-25 05:49:52
http://reply.papertrans.cn/28/2707/270633/270633_21.png一小块 发表于 2025-3-25 08:04:50
http://reply.papertrans.cn/28/2707/270633/270633_22.png极端的正确性 发表于 2025-3-25 13:14:12
Measurement of peroxisomal fatty acid ,-oxidation in cultured human skin fibroblasts, postnatal and prenatal diagnosis of these disorders. In this paper we describe a straightforward and accurate assay method to measure the .-oxidation of palmitic acid (C.), hexacosanoic acid (C.) and pristanic acid in intact fibroblasts.庇护 发表于 2025-3-25 18:06:59
http://reply.papertrans.cn/28/2707/270633/270633_24.png钩针织物 发表于 2025-3-26 00:01:01
Practical guide for morphometry of human peroxisomes on electron micrographs,red to control values. Results from 19 patients with loss of peroxisomal functions are listed. In many patients alterations in peroxisomal morphometric features are found. A brief guideline for interpreting morphometric data is included. Diagnostically relevant morphometric alterations are summarized.Radiation 发表于 2025-3-26 03:15:19
https://doi.org/10.1007/978-3-031-20343-5asma and fibroblasts. A survey is given of the concentrations of very long-chain fatty acids, pristanic and phytanic acid in plasma and fibroblasts from control subjects and all patients investigated so far in our laboratory.considerable 发表于 2025-3-26 07:08:37
http://reply.papertrans.cn/28/2707/270633/270633_27.png不妥协 发表于 2025-3-26 10:50:43
http://reply.papertrans.cn/28/2707/270633/270633_28.pngALIAS 发表于 2025-3-26 16:06:05
http://reply.papertrans.cn/28/2707/270633/270633_29.png关心 发表于 2025-3-26 19:01:21
https://doi.org/10.1007/978-3-031-20343-5somal patients, although it is within normal limits in erythrocytes. Patients with X-linked adrenoleukodystrophy (X-ALD) or adreno-myeloneuropathy (AMN) have a normal DHA and AA content in both plasma and erythrocytes, unless they receive extremely low-PUFA diets.